–Kayser-Fleischer rings are 1-3 mm and consist of copper
granules in the stromal layer of the eye.
–Color changes are visible only in the Descemet membrane
and typically are described as a golden brown, brownish green, bronze, or
tannish green color seen in the limbic area of the eye.
–No visual impairments are associated with the color
changes, which may be detected with the naked eye, although slit lamp
examination is mandatory for confirmation.
–KF rings are seen in 90% of children with neurological
symptoms, 50-60% without neurological symptoms and in 10% of siblings with
asymptomatic disease.
–KF rings start as a small crescent at the top of the
limbus and spread inferiorly then laterally and finally medially to become
circumferential.
–The rings fade and disappear with appropriate chelation
therapy in 3-5 years in the reverse order of appearance.
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