Renal disease
–The product of the WD gene is expressed in renal tissue, but whether the renal symptoms are primary or secondary to release of copper from the liver is unknown.
–
–Renal complications tend to be functional changes unrelated to identifiable histologic findings.
–
–Rarely, patients with WD develop renal stones and associated symptoms. Renal stones are precipitated by hypercalciuria and poor urine acidification. Therapy with copper-chelating agents can improve renal function
•