 |
|
|
|
|
|
| • |
Clinical
evaluation, liver function tests, 24 hour
|
|
urinary
copper, KF rings must be monitored six
|
|
monthly
initially and yearly thereafter.
|
|
|
| • |
Scholastic
and vocational rehabilitation is
|
|
required
for neurological handicaps along with
|
|
considerations
for social problem of costly
|
|
treatment.
|
|
| • |
Liver
transplant is indicated in patients with WD
|
|
with
fulminant hepatic failure and/or disease
|
|
that
is worsening despite chelation therapy.
|
|
Prognostic criteria has been set for patients
|
|
presenting
with fulminant hepatitis.
|
|
|
| • |
Sibling
evaluation is mandatory for occult WD or
|
|
carrier
status of WD gene.
|
|